特发性肺纤维化(IPF)是一种病因不明的慢性间质性肺病(ILD),该病在放射学和病理组织学上表现为普通型间质性肺炎,并伴有肺实质纤维化和过度胶原沉积[1,2]。
参考文献
[1]KingTEJr,PardoA,SelmanM.Idiopathicpulmonaryfibrosis[J].Lancet,,():-61.
[2]SelmanM,KingTE,PardoA.Idiopathicpulmonaryfibrosis:prevailingandevolvinghypothesesaboutitspathogenesisandimplicationsfortherapy[J].AnnInternMed,,(2):-51.
[3]WhiteES,LazarMH,ThannickalVJ.Pathogeneticmechanismsinusualinterstitialpneumonia/idiopathicpulmonaryfibrosis[J].JPathol,,(3):-54.
[4]程洁,毛燕君,鲁敏,等.特发性肺纤维化的非药物治疗进展[J].国际呼吸杂志,8,38(15):-.
[5]RaghuG,Remy-JardinM,RicheldiL,etal.IdiopathicPulmonaryFibrosis(anUpdate)andProgressivePulmonaryFibrosisinAdults:AnOfficialATS/ERS/JRS/ALATClinicalPracticeGuideline[J].AmJRespirCritCareMed,,(9):e18-e47.
[6]叶俏,代华平.特发性肺纤维化诊断和治疗中国专家共识[J].中华结核和呼吸杂志,6,39(06):-.
来源:医院药事部